Dicephalus dipus dibrachius twins: report of an autopsy case

Autopsy And Case Reports

Av. Prof. Lineu Prestes, 2565
São Paulo / SP
Site: http://www.autopsyandcasereports.org
Telefone: (11) 3091-9448
ISSN: 22361960
Editor Chefe: Maria Claudia Nogueira Zerbini
Início Publicação: 28/02/2011
Periodicidade: Trimestral
Área de Estudo: Medicina

Dicephalus dipus dibrachius twins: report of an autopsy case

Ano: 2014 | Volume: 4 | Número: 2
Autores: C. C. Oliveira, C. A. Rainho, M. A. C. Domingues
Autor Correspondente: C. C. Oliveira | [email protected]

Palavras-chave: autopsy, twins conjoined, cytogenetics, embryology, fetal diseases

Resumos Cadastrados

Resumo Inglês:

Dicephalus dipus dibrachius twins are a rare form of conjoined twins. An autopsy of conjoined dicephalus twins is reported. The diagnosis was performed during the pregnancy and the family received a judicial authorization for termination of pregnancy. The preterm newborn progressed to cardiac arrest and died following a court order to terminate the pregnancy. The conceptus presented two arms, two legs, a trunk, two heads, and a single umbilical cord. The two spinal columns presented vertebral fusion in the sacral region. The heart exhibited complex malformations. The external genitalia were
female; and cytogenetic analysis confirmed female sex (46, XX). This analysis also corroborated the etiopathogenic hypotheses described for this abnormality, which proposes failures in embryonic formation rather than specific chromosomal alterations. Current identification of cases by ultrasound permits medical management and multidisciplinary action with the family, enabling the legal termination of pregnancy.