Müllerian adenosarcoma is a rare, mixed tumor that can occur throughout the female genital tract, but is most commonly
found in the uterus. Ovarian adenosarcoma is rarer and has a poorer prognosis than uterine adenosarcoma. Data on the
clinicopathological features of ovarian adenosarcoma are limited, and, due to its rarity, the management is controversial. The
authors report a case of a 25-year-old patient who presented with recurrent abdominal pain. Sonography and laparotomy
showed an ovarian cyst, and pathologic examination confirmed the diagnosis of cystic low-grade adenosarcoma. The
patient remains free of recurrence 6 months after diagnosis. The authors call attention to the differential diagnosis of
ovarian masses, especially in young patients, and to the lack of evidence on the management of this neoplasm in the
literature.
